Adrenal gland and paraganglia
WHO classification of tumors
Tumors of the adrenal medulla


Topic Completed: 1 July 2018

Revised: 4 June 2019

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PubMed Search: Adrenal medulla tumors - WHO classification

Andrey Bychkov, M.D., Ph.D.
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Cite this page: Bychkov A. Tumors of the adrenal medulla - WHO classification. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/adrenalmedullawho.html. Accessed July 18th, 2019.
WHO (2017)
  • Tumors of the adrenal medulla and extra-adrenal paraganglia ICD 0 codes
    • Pheochromocytoma 8700/3
    • Extra-adrenal paragangliomas
      • Head and neck paragangliomas
        • Carotid body paraganglioma 8692/3
        • Jugulotympanic paraganglioma8690/3
        • Vagal paraganglioma8693/3
        • Laryngeal paraganglioma8693/3
      • Sympathetic paraganglioma 8693/3
    • Neuroblastic tumors of the adrenal gland
      • Neuroblastoma 9500/3
      • Ganglioneuroblastoma, nodular 9490/3
      • Ganglioneuroblastoma, intermixed 9490/3
      • Ganglioneuroma9490/0
    • Composite pheochromocytoma 8700/3
    • Composite paraganglioma8693/3
  • ICD 0 note: the first four digits indicate the specific histological term; the fifth digit after the slash (/) is the behavior code, including /0 for benign tumors, /1 for unspecified, borderline or uncertain behavior, /2 for carcinoma in situ and grade III intraepithelial neoplasia (not used for adrenal tumors), and /3 for malignant tumors
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