Adrenal gland and paraganglia
Tumors of the adrenal medulla
World Health Organization (WHO) classification

Author: Andrey Bychkov, M.D., Ph.D.

Revised: 8 January 2018, last major update July 2018

Copyright: (c) 2002-2017, PathologyOutlines.com, Inc.

PubMed Search: Adrenal medulla tumors - WHO classification

Cite this page: Bychkov, A. Tumors of the adrenal medulla - WHO classification. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/adrenalmedullawho.html. Accessed July 21st, 2018.
WHO (2017)
  • Tumors of the adrenal medulla and extra-adrenal paraganglia ICD 0 codes
    • Pheochromocytoma 8700/3
    • Extra-adrenal paragangliomas
      • Head and neck paragangliomas
        • Carotid body paraganglioma 8692/3
        • Jugulotympanic paraganglioma8690/3
        • Vagal paraganglioma8693/3
        • Laryngeal paraganglioma8693/3
      • Sympathetic paraganglioma 8693/3
    • Neuroblastic tumors of the adrenal gland
      • Neuroblastoma 9500/3
      • Ganglioneuroblastoma, nodular 9490/3
      • Ganglioneuroblastoma, intermixed 9490/3
      • Ganglioneuroma9490/0
    • Composite pheochromocytoma 8700/3
    • Composite paraganglioma8693/3
  • ICD 0 note: the first four digits indicate the specific histological term; the fifth digit after the slash (/) is the behavior code, including /0 for benign tumors, /1 for unspecified, borderline or uncertain behavior, /2 for carcinoma in situ and grade III intraepithelial neoplasia (not used for adrenal tumors), and /3 for malignant tumors