Desmoplastic small cell tumor

Bone
Other tumors of bone
Desmoplastic small cell tumor

Author: Nat Pernick, M.D. (see Authors page)

Revised: 20 October 2016, last major update June 2005

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PubMed search: desmoplastic small cell tumor [title] bone

Table of Contents

Definition / general | Case reports | Positive stains | Molecular / cytogenetics description

Cite this page: Desmoplastic small cell tumor. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/bonedesmoplasticsmallcell.html. Accessed July 14th, 2017.

Definition / general

High grade malignant neoplasm, usually of peritoneum or other serosal surfaces, rarely in bone or soft tissue

Case reports

34 year old man with hand mass and later lung metastases (Am J Surg Pathol 1999;23:1408)

Positive stains

CAM5.2, AE1 / AE3, EMA, desmin, chromogranin, synaptophysin

Molecular / cytogenetics description

EWS / WT1 gene fusion