Bone
Fibrous and fibroosseous tumors of bone
Monostotic

Author: Nat Pernick, M.D. (see Authors page)

Revised: 20 July 2018, last major update August 2013

Copyright: (c) 2003-2018, PathologyOutlines.com, Inc.

PubMed Search: Monostotic fibrous dysplasia

Related topics: Fibrous dysplasia, Polyostotic, McCune-Albright syndrome, Mazabraud syndrome, Fibrous dysplasia protuberans

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Cite this page: Pernick, N. Monostotic. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/bonefibrousdysplasiamonostotic.html. Accessed August 18th, 2019.
Definition / general
  • 80% of cases, teenagers / young adults, no gender preference; resolves after puberty, doesn't become polyostotic
  • Asymptomatic unless involves face (causes disfigurement)
  • Malignant transformation in 0.5%
  • Sites: ribs, femur (causes crook neck deformity of neck resembling candy cane, also called Shepherd's crook), tibia, jaw
Radiology description
  • Incidental lucent or ground glass lesion replacing bony spongiosa with well defined and occasionally sclerotic margins
  • Thin cortex
  • Shepherd's crook deformity
Additional references
  • Conservative surgery if symptoms (limited resection, curettage, partial removal in jaw to cure deformity)
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