Congenital anomalies

Author: Elliot Weisenberg, M.D. (see Authors page)

Revised: 10 January 2018, last major update September 2012

Copyright: (c) 2003-2018,, Inc.

PubMed Search: Esophageal stenosis[TI] pathology

Cite this page: Weisenberg, E. Stenosis. website. Accessed March 19th, 2018.
Definition / general
  • Fibrous thickening of esophageal wall, particularly the submucosa, with atrophy of muscularis propria, thin and ulcerated lining epithelium
  • Congenital cases defined as intrinsic alteration of esophageal wall due to ectopic tracheobronchial tissue, membranous diaphragm, muscular hypertrophy or diffuse fibrosis of submucosa (Pediatr Surg Int 2001;17:188)
  • Associated with esophageal atresia or other congenital malformations in 17 - 33%
  • Acquired cases due to severe esophageal injury with scarring (reflux, radiation, scleroderma, caustic injury); associated with progressive dysphagia, may cause total obstruction
Case reports