Orbit and optic nerve
Hemangioma of orbit

Topic Completed: 1 March 2014

Minor changes: 4 April 2019

Copyright: 2004-2019, PathologyOutlines.com, Inc.

PubMed Search: Hemangioma [title] orbit

Nat Pernick, M.D.
Page views in 2019: 416
Page views in 2020 to date: 124
Cite this page: Pernick N. Orbit and optic nerve: hemangioma of orbit. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/eyeorbithemangioma.html. Accessed May 28th, 2020.
Definition / general
  • Common
  • More common than lymphangioma
  • Usually cavernous, in young adults in retrobulbar space
  • Benign but slowly progressive
  • May cause chorioretinal stria or folds
Clinical features
  • Infants:
    • Soft, blue, compressible
    • Diffuse throughout orbit, may extend into eyelids
    • Usually regress by age 4, difficult to excise
    • Respond to short course of systemic steroids or radiotherapy
  • Adults:
    • Encapsulated, close to back of eye
    • Can usually shell out tumors
Radiology images

AFIP images
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CT scan shows intraconal,
well circumscribed ovoid
retrobulbar tumor

Case of the Week #301
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Case reports
  • 45 year old woman with 6 month history of blurry vision and proptosis of the right eye (Case of the Week #301)
Microscopic (histologic) description
  • Encapsulated, large cavernous vascular channels or spaces separated by scant connective tissue stroma
  • Spaces lined by single layer of endothelial cells with variable smooth muscle in walls
  • Infants:
    • Unencapsulated
    • Usually capillary type with thin walled vessels
    • May have prominent mitotic activity
  • Adults:
    • Usually cavernous type with large, blood filled, endothelium lined channels
    • Thrombi often present, may calcify
Microscopic (histologic) images

AFIP images

Cavernous hemangioma
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Well circumscribed
tumor composed of
dilated blood vessels

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Thick walled dilated blood vessels

Case of the Week #301
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