Von Hippel-Lindau disease of retina

Author: Nat Pernick, M.D. (see Authors page)

Revised: 22 May 2018, last major update February 2014

Copyright: (c) 2004-2018, PathologyOutlines.com, Inc.

PubMed Search: Von Hippel-Lindau disease [title] retina

Cite this page: Pernick, N. Retina: von Hippel-Lindau disease of retina. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/eyeretinavhl.html. Accessed November 17th, 2018.
Definition / general
  • Also called angiogliomatosis
  • Abnormally large tortuous arteries and veins leading to a retinal nodule composed of vascular, endothelial and glial tissue
  • Associated with retinal detachment and vitreous disturbance
Microscopic (histologic) images

Images hosted on PathOut server:
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Lesion adjacent to
optic nerve head
with osseous
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Vascular proliferation with vacuolated stromal cells