von Hippel-Lindau disease of retina

Topic Completed: 1 February 2014

Minor changes: 5 April 2019

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PubMed Search: von Hippel-Lindau disease [title] retina

Nat Pernick, M.D.
Page views in 2019: 89
Page views in 2020 to date: 25
Cite this page: Pernick N. Retina: von Hippel-Lindau disease of retina. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/eyeretinavhl.html. Accessed May 28th, 2020.
Definition / general
  • Also called angiogliomatosis
  • Abnormally large tortuous arteries and veins leading to a retinal nodule composed of vascular, endothelial and glial tissue
  • Associated with retinal detachment and vitreous disturbance
Microscopic (histologic) images

AFIP images
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Lesion adjacent to
optic nerve head
with osseous
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Vascular proliferation with vacuolated stromal cells

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