General
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• See also malignant fibrous histiocytoma (some authors consider them the same entity)
• Rare, but common subtype of sarcoma in heart (Histopathology 1999;34:295)

Case reports
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• 3 year old boy with mitral valve tumor (J Cardiovasc Surg (Torino) 2003;44:621)
• 13 year old girl with widespread disease (Clin Med Res 2003;1:233)
• 33 year old woman with clinical atrial myxoma (Yonsei Med J 2003;44:530)
• 37 year old woman with left atrial mass (Yonsei Med J 2007;48:131)

Gross images
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One year old girl with congestive heart failure

Involving left atrial appendage and mitral valve

70 year old man with pedunculated mass attached to infundibulum (base of pulmonary artery)

28 year old woman with left atrial mass

Micro images
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Undifferentiated pleomorphic and giant cells

Epithelioid features

Small round cells in myxoid background

Small round cell tumor of right atrium

Electron microscopy images
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Bipolar cells with tapering cell processes

Abundant rough endoplasmic reticulum and well-formed intercellular junctions

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