Kidney nontumor
Inherited glomerular diseases
Congenital nephrotic syndrome


Topic Completed: 2 April 2012

Revised: 26 February 2019

Copyright: 2002-2019, PathologyOutlines.com, Inc.

PubMed Search: Congenital nephrotic syndrome [title] "loattrfree full text"[sb]

See also: Diffuse mesangial sclerosis, Finnish type

Nikhil Sangle, M.D.
Page views in 2019: 360
Page views in 2020 to date: 11
Cite this page: Sangle N. Congenital nephrotic syndrome. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/kidneycongenitalnephroticsyndrome.html. Accessed January 18th, 2020.
Definition / general
  • Heterogenous conditions with nephrotic syndrome within first 3 months of life
  • Onset between 3 - 12 months is called infantile nephrotic syndrome
  • No response to steroids or immunosuppressive therapy
  • Divided into Finnish type and diffuse mesangial sclerosis but may also be a part of a more generalized syndrome or caused by a perinatal infection (Pediatr Nephrol 2009;24:2121)
Diagrams / tables

Images hosted on other servers:

Normal glomerular capillary and capillary wall

Treatment
  • Renal transplant
Differential diagnosis
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