Cite this page: Sangle, N. Congenital nephrotic syndrome. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/kidneycongenitalnephroticsyndrome.html. Accessed February 18th, 2018.
Definition / general
- Heterogenous conditions with nephrotic syndrome within first 3 months of life
- Onset between 3 - 12 months is called infantile nephrotic syndrome
- No response to steroids or immunosuppressive therapy
- Divided into Finnish type and diffuse mesangial sclerosis but may also be a part of a more generalized syndrome or caused by a perinatal infection (Pediatr Nephrol 2009;24:2121)
- Renal transplant