Liver and intrahepatic bile ducts - nontumor
Vascular disorders
Hereditary hemorrhagic telangiectasia

Author: Komal Arora, M.D. (see Authors page)

Revised: 9 November 2017, last major update May 2012

Copyright: (c) 2002-2017, PathologyOutlines.com, Inc.

PubMed Search: Hereditary hemorrhagic telangiectasia[TI] liver[TI]

Cite this page: Arora, K. Hereditary hemorrhagic telangiectasia. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/liverHHT.html. Accessed December 14th, 2017.
Definition / general
  • Also called Osler-Weber-Rendu disease
Microscopic (histologic) description
  • Thin walled portal vessels may extend into parenchyma and become associated with fibrosis
  • Intrahepatic hypervascularization, enlarged common hepatic artery
  • Focal nodular hyperplasia and nodular regenerative hyperplasia are common