Liver and intrahepatic bile ducts - nontumor
Developmental anomalies / cysts
Choledochal cyst

Author: Komal Arora, M.D. (see Authors page)

Revised: 25 October 2017, last major update April 2012

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PubMed Search: Liver choledochal cyst[TI] free full text[sb]

Cite this page: Arora, K. Choledochal cyst. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/livercholedochalcyst.html. Accessed December 12th, 2017.
Definition / general
  • Cystic dilatations of the biliary tree; can involve the extrahepatic biliary radicles, the intrahepatic biliary radicles or both
  • Classified into 5 types (Am J Surg 1977;134:263)
  • Classically presents with pain, right upper quadrant mass and jaundice, particularly in children
  • Cholangitis symptoms may predominate in adults
  • Usually women
  • 14% develop adenocarcinoma with increasing age
Diagrams / tables

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Choledochal cyst classification

Clinical images

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Intraoperative view of choledochal cyst

Gross description
  • Often huge cysts
Microscopic (histologic) description
  • Thick fibrous wall, often inflamed
  • Discontinuous columnar epithelium; variable squamous metaplasia (Can J Surg 2009;52:434)