Liver and intrahepatic bile ducts-nontumor
Reviewers: Komal Arora, M.D. (see Reviewers page)
Revised: 9 April 2012, last major update April 2012
Copyright: (c) 2004-2012, PathologyOutlines.com, Inc.
● Cystic dilatations of the biliary tree; can involve the extrahepatic biliary radicles, the intrahepatic biliary radicles, or both
● Classified into 5 types (Am J Surg 1977;134:263)
● Classically presents with pain, right upper quadrant mass and jaundice, particularly in children
● Cholangitis symptoms may predominate in adults
● Usually women
● 14% develop adenocarcinoma with increasing age
● Often huge cysts
Choledochal cyst classification
Intraoperative view of choledochal cyst
● Thick fibrous wall, often inflamed
● Discontinuous columnar epithelium; variable squamous metaplasia (Can J Surg 2009;52:434)
Lining of choledochal cyst
End of Liver and intrahepatic bile ducts-nontumor > Developmental anomalies/cysts > Choledochal cyst
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