Liver and intrahepatic bile ducts - nontumor
Developmental anomalies / cysts
Multiple hilar cysts



Topic Completed: 1 April 2012

Revised: 22 January 2019, last major update April 2012

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PubMed Search: Multiple hilar cysts


Komal Arora, M.D.
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Cite this page: Arora K. Multiple hilar cysts. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/livermultiplehilarcyst.html. Accessed October 16th, 2019.
Definition / general
  • Arise from peribiliary glands surrounding extrahepatic and large intrahepatic bile ducts in hilum (J Gastroenterol Hepatol 1997;12:137)
  • Cysts are incidental finding in 20% of autopsies
  • May compress adjacent bile duct; also associated with cirrhosis and portal vein thrombosis
Gross description
  • Up to 2 cm, unilocular with clear serous fluid, if multiple may make liver appear spongy
Microscopic (histologic) description
  • Lined by columnar to cuboidal epithelium with mild chronic inflammatory infiltrate, fibrosis, fibrous obliteration of small veins; occasional hyperplasia
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