Liver and intrahepatic bile ducts - nontumor
Developmental anomalies / cysts
Multiple hilar cysts

Author: Komal Arora, M.D. (see Authors page)

Revised: 25 October 2017, last major update April 2012

Copyright: (c) 2002-2017,, Inc.

PubMed Search: Multiple hilar cysts

Cite this page: Arora, K. Multiple hilar cysts. website. Accessed July 21st, 2018.
Definition / general
  • Arise from peribiliary glands surrounding extrahepatic and large intrahepatic bile ducts in hilum (J Gastroenterol Hepatol 1997;12:137)
  • Cysts are incidental finding in 20% of autopsies
  • May compress adjacent bile duct; also associated with cirrhosis and portal vein thrombosis
Gross description
  • Up to 2 cm, unilocular with clear serous fluid, if multiple may make liver appear spongy
Microscopic (histologic) description
  • Lined by columnar to cuboidal epithelium with mild chronic inflammatory infiltrate, fibrosis, fibrous obliteration of small veins; occasional hyperplasia