Congenital anomalies

Author: Deepali Jain, M.D. (see Authors page)

Revised: 7 December 2017, last major update August 2012

Copyright: (c) 2002-2017,, Inc.

PubMed Search: Agenesis[TI] pancreas[TI]

Cite this page: Jain, D. Agenesis. website. Accessed October 23rd, 2018.
Definition / general
  • Extremely rare anomaly
  • Associated with severe intrauterine growth restriction, early onset of diabetes mellitus without ketoacidosis, failure to thrive due to pancreatic insufficiency and malformations of the biliary system and the heart (Klin Padiatr 2005;217:76)
  • High mortality
  • Agenesis of dorsal pancreas is also rare; either partial or complete (JOP 2012;13:108); associated with polysplenia syndrome (Br J Radiol 2011;84:e217)

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Various images

Clinical images

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Intraoperative image of dorsal agenesis