Cite this page: Jain, D. Agenesis. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/pancreasagenesis.html. Accessed April 21st, 2018.
Definition / general
- Extremely rare anomaly
- Associated with severe intrauterine growth restriction, early onset of diabetes mellitus without ketoacidosis, failure to thrive due to pancreatic insufficiency and malformations of the biliary system and the heart (Klin Padiatr 2005;217:76)
- High mortality
- Agenesis of dorsal pancreas is also rare; either partial or complete (JOP 2012;13:108); associated with polysplenia syndrome (Br J Radiol 2011;84:e217)