Other malignancies

Topic Completed: 1 March 2017

Revised: 28 February 2019

Copyright: 2003-2019,, Inc.

PubMed Search: prostatic PEComa
Page views in 2018: 194
Page views in 2019 to date: 90
Cite this page: Arora K, Iczkowski KA. PEComa. website. Accessed May 19th, 2019.
Definition / general
  • Perivascular epithelioid cell tumors (PEComas) include clear cell "sugar" tumor of lung, lymphangioleiomyomatosis, angiomyolipoma (see Soft Tissue chapter)
Case reports
Microscopic (histologic) description
  • Epithelioid cells with clear / granular cytoplasm in perivascular distribution
Microscopic (histologic) images

Images hosted on other servers:

Various images

Positive stains
Negative stains
Electron microscopy description
  • May have premelanosomes
Electron microscopy images

Images hosted on other servers:

Malignant PEComa

Differential diagnosis
  • Clear cell sarcoma of soft parts: no vascular stroma, no perivascular arrangement of tumor cells, S100+
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