Other malignancies

Authors: Kenneth Iczkowski, M.D., Komal Arora, M.D. (see Authors page)

Revised: 14 March 2017, last major update March 2017

Copyright: (c) 2003-2017,, Inc.

PubMed Search: prostatic PEComa

Cite this page: PEComa. website. Accessed October 18th, 2018.
Definition / general
  • Perivascular epithelioid cell tumors (PEComas) include clear cell "sugar" tumor of lung, lymphangioleiomyomatosis, angiomyolipoma (see Soft Tissue chapter)
Case reports
Microscopic (histologic) description
  • Epithelioid cells with clear / granular cytoplasm in perivascular distribution
Microscopic (histologic) images
Images hosted on other servers:

Various images

Positive stains
Negative stains
Electron microscopy description
  • May have premelanosomes
Electron microscopy images
Images hosted on other servers:

Malignant PEComa

Differential diagnosis
  • Clear cell sarcoma of soft parts: no vascular stroma, no perivascular arrangement of tumor cells, S100+