Skin melanocytic tumor
Other pigmented lesions and disorders of pigmentation
Linear and whorled nevoid hypermelanosis

Author: Christopher Hale, M.D.

Revised: 10 September 2018, last major update April 2013

Copyright: (c) 2002-2018, PathologyOutlines.com, Inc.

PubMed Search: Linear and whorled nevoid hypermelanosis

Cite this page: Hale, C.S. Linear and whorled nevoid hypermelanosis. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/skintumormelanocyticlinearandwhorled.html. Accessed October 16th, 2018.
Definition / general
  • Rare skin disorder, often in first weeks of life, with swirls and streaks of macular hyperpigmentation along lines of Blaschko (Wikipedia)
  • Usually not associated with other abnormalities (Pediatr Dermatol 2007;24:205)
Diagrams / tables

Images hosted on other servers:

Lines of Blaschko

Clinical features
  • Swirls and whorls of hyperpigmented macules in reticulate pattern along Blaschko lines
Case reports
Treatment
  • No satisfactory treatment
Clinical images

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Whorled pattern over trunk (fig. 2)

Macular hyperpigmentation

Microscopic (histologic) description
  • Epidermal melanosis
  • No pigment incontinence or melanophages
Microscopic (histologic) images

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Epidermal hypermelanosis

Diffuse melanosis (fig. 1)