Soft tissue
Low / intermediate grade vascular tumors
Kaposiform hemangioendothelioma

Author: Vijay Shankar, M.D.

Revised: 31 January 2018, last major update November 2012

Copyright: (c) 2002-2018, PathologyOutlines.com, Inc.

PubMed search: Kaposiform [title] hemangioendothelioma

Related topics: Hemangioendothelioma

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Cite this page: Shankar, V. Kaposiform hemangioendothelioma. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/softtissuehemangioendotheliomakaposiform.html. Accessed June 16th, 2019.
Definition / general
  • Rare, locally aggressive; tumor of infants and children; affects skin (75%), retroperitoneum (18%), bone
  • Death due to extensive disease and severe coagulopathy (Kasabach-Merritt syndrome), although no metastatic potential (Mod Pathol 2001;14:1087)
  • Usually initial tumor is cutaneous
Case reports
Clinical images
Images hosted on PathOut server:

Courtesy of Dr. Mark R. Wick



Images hosted on other servers:

Tonsillar mass

Microscopic (histologic) description
  • Infiltrating nodules and sheets of compact spindle cells with slit-like lumina
Microscopic (histologic) images
Images hosted on PathOut server:

Courtesy of Dr. Mark R. Wick



Case of the Week #401:

Low power view

20x

CD31 (20x)

CD34

SMA

Vimentin



Images hosted on other servers:

Glomeruloid nests of spindled and epithelioid cells

"Cannon ball" appearance

Slit-like lumens

VEGFR3+


Tonsillar mass

Differential diagnosis
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