Cite this page: Shankar V. Port wine stain. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/softtissuevascularectasiasportwine.html. Accessed June 20th, 2019.
Definition / general
- Type of nevus flammeus
- May grow proportionately with the child and thicken the skin surface
- Those in distribution of trigeminal nerve are associated with Sturge-Weber syndrome (encephalotrigeminal angiomatosis), a rare congenital disorder with venous angiomatous masses in leptomeninges over cortex, ipsilateral port wine nevi, intellectual disability, seizures, hemiplegia, skull radiopacities
- Attributed to faulty development of mesodermal and ectodermal elements