Congenital anomalies
Asplenia (congenital absence of spleen)

Author: Jaleh Mansouri, M.D. (see Authors page)

Revised: 28 February 2018, last major update October 2012

Copyright: (c) 2003-2018, PathologyOutlines.com, Inc.

PubMed Search: Asplenia congenital absence of spleen

Cite this page: Mansouri, J. Asplenia (congenital absence of spleen). PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/spleenasplenia.html. Accessed July 17th, 2018.
Definition / general
  • Rare, associated with cardiac malformations (80%, usually involving atrioventricular endocardial cushion and ventricular outflow tract), situs inversus, anomalies of blood vessels, lung, abdominal viscera
  • Can present with pneumococcal sepsis (OPSI)
Case reports