Congenital anomalies

Author: Jaleh Mansouri, M.D. (see Authors page)

Revised: 28 February 2018, last major update October 2012

Copyright: (c) 2003-2018, PathologyOutlines.com, Inc.

PubMed Search: Hyposplenism[TI]

Table of Contents
Definition / general
Cite this page: Mansouri, J. Hyposplenism. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/spleenhyposplenism.html. Accessed July 17th, 2018.
Definition / general
  • Atrophy of spleen with concomitant compromised splenic function (Lancet 2011;378:86)
  • Usually acquired but rare congenital forms exist (isolated congenital hyposplenia, Ivemark syndrome, hypoparathyroidism syndrome, autoimmune polyendocrinopathy candidiasis ectodermal dystrophy [APECED] syndrome, Stormorken syndrome)