Congenital anomalies

Author: Jaleh Mansouri, M.D. (see Authors page)

Revised: 28 February 2018, last major update October 2012

Copyright: (c) 2003-2018, PathologyOutlines.com, Inc.

PubMed Search: Polysplenia[TI] spleen full text[sb]

Cite this page: Mansouri, J. Polysplenia. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/spleenpolysplenia.html. Accessed August 16th, 2018.
Definition / general
  • Multiple spleens, found as part of heterotaxy syndromes (malpositioning of organs on opposite side of body, e.g. situs inversus)
  • Associated with extrahepatic biliary atresia (Arch Pathol Lab Med 1980;104:212), cardiac abnormalities and developmental anomalies of pancreas, portal vein, inferior vena cava
Case reports
  • 62 year old woman with polysplenia with agenesis of dorsal pancreas and preduodenal portal vein presenting with obstructive jaundice (Br J Radiol 2011;84:e217)