Congenital anomalies
Splenic gonadal fusion

Topic Completed: 1 October 2012

Revised: 18 March 2019

Copyright: 2003-2019, PathologyOutlines.com, Inc.

PubMed Search: Splenic gonadal fusion[TIAB]

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Cite this page: Mansouri J. Splenic gonadal fusion. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/spleensplenicgonadalfusion.html. Accessed October 18th, 2019.
Definition / general
  • Rare congenital anomaly in which ectopic splenic tissue unites with a gonad (< 200 cases reported)
  • Continuous or discontinuous
  • Continuous: spleen connected to ectopic splenic mass by cord of splenic and fibrous tissue
  • Discontinuous: no connection between spleen and ectopic splenic mass
  • 20% of continuous types associated with other congenital defects, including peromelus (fetus with malformed limbs) and micrognathia; also testicular ectopia, inguinal hernia
  • 90% in males; usually left sided; usually less than 20 years old
  • Technetium Tc 99m sulfur colloid scan
Case reports
  • Surgical excision of ectopic splenic tissue to prevent testicular atrophy, torsion or infarction and preserve fertility
Gross description
  • Ectopic splenic tissue is well demarcated from gonad, only rarely is intermingling of tissue
Gross / microscopic (histologic) images

Case of the Week #309

Various images

Images hosted on other servers:

1: red brown firm tumor; 2: tumor is separated from testicle
without invasion; 3: tumor has scattered lymphoid follicles
with germinal centers; 4: composed of loose reticular
tissue with abundant capillaries and venous sinuses

With nonseminomatous germ
cell testicular tumor composed
of embryonal carcinoma
and yolk sac tumor

Microscopic (histologic) description
  • Normal splenic parenchyma but may have thrombosis, calcification, fibrosis, fat degeneration, hemosiderin deposits
  • Testicular tissue may be normal but may have atrophy or fibrosis of seminiferous tubules, increased Leydig cells, thrombosis of spermatic vessels or testicular tumors
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