Skin nontumor
Pigmentary disorders
Linear and whorled nevoid hypermelanosis
Author: Christopher S. Hale, M.D.
Last author update: 1 April 2013
Last staff update: 28 August 2020
Copyright: 2002-2023, PathologyOutlines.com, Inc.
PubMed Search: Linear and whorled nevoid hypermelanosis
Table of Contents
Definition / general | Diagrams / tables | Clinical features | Case reports | Treatment | Clinical images | Microscopic (histologic) description | Microscopic (histologic) imagesCite this page: Hale CS. Linear and whorled nevoid hypermelanosis. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/skintumormelanocyticlinearandwhorled.html. Accessed April 2nd, 2023.
Definition / general
- Rare skin disorder, often in first weeks of life, with swirls and streaks of macular hyperpigmentation along lines of Blaschko (Wikipedia)
- Usually not associated with other abnormalities (Pediatr Dermatol 2007;24:205)
Diagrams / tables
Images hosted on other servers:
Lines of Blaschko
Clinical features
- Swirls and whorls of hyperpigmented macules in reticulate pattern along Blaschko lines
Case reports
- 3 month old boy with diffuse hyperpigmentation (J Pediatr 2012;160:171)
- 7 year old boy with trisomy 20 mosaicism (Pediatr Dermatol 2004;21:636)
- 20 year old man with widespread involvement (Dermatol Online J 2007;13:23)
- Familial case of 33 year old woman and her 3 month old daughter (J Am Acad Dermatol 1994;30:831)
Treatment
- No satisfactory treatment
Clinical images
Images hosted on other servers:
Whorled pattern over trunk (fig. 2)
Macular hyperpigmentation
Microscopic (histologic) description
- Epidermal melanosis
- No pigment incontinence or melanophages
Microscopic (histologic) images
Images hosted on other servers:
Epidermal hypermelanosis
Diffuse melanosis (fig. 1)
