Soft tissue
Vascular
Intermediate (locally aggressive / rarely metastasizing)
Kaposiform hemangioendothelioma


Topic Completed: 1 November 2012

Minor changes: 19 April 2021

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PubMed search: Kaposiform [title] hemangioendothelioma

Vijay Shankar, M.D.
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Cite this page: Shankar V. Kaposiform hemangioendothelioma. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/softtissuehemangioendotheliomakaposiform.html. Accessed May 11th, 2021.
Definition / general
  • Rare, locally aggressive; tumor of infants and children; affects skin (75%), retroperitoneum (18%), bone
  • Death due to extensive disease and severe coagulopathy (Kasabach-Merritt syndrome), although no metastatic potential (Mod Pathol 2001;14:1087)
  • Usually initial tumor is cutaneous
Case reports
Clinical images

Contributed by Mark R. Wick, M.D.


Images hosted on other servers:

Tonsillar mass

Microscopic (histologic) description
  • Infiltrating nodules and sheets of compact spindle cells with slit-like lumina
Microscopic (histologic) images

Contributed by Mark R. Wick, M.D.



Case #401

Low power view

20x


CD31 (20x)

CD34

SMA

Vimentin



Images hosted on other servers:

Glomeruloid nests of spindled and epithelioid cells


Tonsillar mass

Differential diagnosis
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