Soft tissue
General
WHO classification-GI mesenchymal tumors
Author: Raul S. Gonzalez, M.D.
Editor-in-Chief: Debra L. Zynger, M.D.
Last author update: 10 December 2020
Last staff update: 23 June 2021
Copyright: 2020, PathologyOutlines.com, Inc.
PubMed Search: WHO classification gastrointestinal mesenchymal
Cite this page: Gonzalez RS. WHO classification-GI mesenchymal tumors. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/softtissuewhoclassificationgi.html. Accessed June 8th, 2023.
Definition / general
- WHO classification of mesenchymal tumors of the digestive system
- First provided in the Digestive System Tumors, 5th edition, published in 2019
WHO (2019)
-
Gastrointestinal stromal tumor ICD-O codes
- Gastrointestinal stromal tumor 8936/3
- Succinate dehydrogenase deficient gastrointestinal stromal tumor
-
Adipose tissue and (myo)fibroblastic tumors ICD-O codes
- Inflammatory myofibroblastic tumor 8825/1
- Epithelioid inflammatory myofibroblastic sarcoma
- Desmoid type fibromatosis 8821/1
- Abdominal fibromatosis 8815/1
- Solitary fibrous tumor, NOS 8815/3
- Solitary fibrous tumor, malignant
- Lipomatous solitary fibrous tumor
- Giant cell angiofibroma 9160/0
- Lipoma, NOS 8850/0
- Angiolipoma, NOS 8861/0
- Plexiform fibromyxoma 8811/0
-
Smooth muscle and skeletal muscle tumors ICD-O codes
- Leiomyoma, NOS 8890/0
- Seedling leiomyomas
- Leiomyomatosis, NOS 8890/1
- Leiomyosarcoma, NOS 8890/3
- Embryonal rhabdomyosarcoma, NOS 8910/3
- Rhabdomyosarcoma, spindle cell / sclerosing type 8912/3
- Alveolar rhabdomyosarcoma 8920/3
-
Vascular and perivascular tumors ICD-O codes
- Hemangioma, NOS 9120/0
- Dieulafoy lesion
- Gastric antral vascular ectasia (GAVE)
- Angiodysplasia
- Anastomosing hemangioma
- Infantile hemangioma
- Diffuse hepatic hemangiomatosis
- Hepatic small vessel neoplasm
- Epithelioid hemangioendothelioma, NOS 9133/3
- Kaposi sarcoma 9140/3
- Angiosarcoma 9120/3
- Epithelioid angiosarcoma
- Glomus tumor, NOS 8711/0
- Glomangiomatosis 8711/1
- Glomus tumor of uncertain malignant potential 8711/1
- Glomus tumor, malignant 8711/3
- Lymphangioma, NOS 9170/0
-
Neural tumors ICD-O codes
- Schwannoma, NOS 9560/0
- Granular cell tumor, NOS 9580/0
- Granular cell tumor, malignant 9580/3
- Perineurioma, NOS 9571/0
- Ganglioneuroma 9490/0
- Ganglioneuromatosis 9491/0
-
Tumors of uncertain differentiation ICD-O codes
- PEComa, benign 8714/0
- Sclerosing PEComa
- Angiomyolipoma 8860/0
- Inflammatory subtype of angiomyolipoma
- PEComa, malignant 8714/3
- Calcifying nested stromal epithelial tumor 8975/1
- Synovial sarcoma, NOS 9040/3
- Synovial sarcoma, monophasic fibrous 9041/3
- Synovial sarcoma, biphasic 9043/3
- Clear cell sarcoma, NOS 9044/3
- Embryonal sarcoma 8991/3
