Small bowel (small intestine)
Malabsorption
Lymphangiectasia

Author: Hanni Gulwani, M.D. (see Authors page)

Revised: 12 February 2018, last major update August 2012

Copyright: (c) 2003-2018, PathologyOutlines.com, Inc.

PubMed Search: Lymphangiectasia[TI] small bowel[TIAB]
Cite this page: Gulwani, H. Lymphangiectasia. PathologyOutlines.com website. http://www.pathologyoutlines.com/topic/smallbowellymphangiectasia.html. Accessed October 16th, 2018.
Definition / general
  • Primary intestinal lymphangiectasia is rare disorder of dilated intestinal lacteals resulting in lymph leakage into the small bowel lumen, causing protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia (Orphanet J Rare Dis 2008;3:5, eMedicine: Intestinal Lymphangiectasia [Accessed 12 February 2018])
  • Dilation of lymphatics in mucosa, submucosa or subserosa
  • Primary: children, due to congenital obstructive defective in lymphatics
  • Secondary: due to constrictive pericarditis, Crohn's (Virchows Arch 2008;452:57), intestinal malignancy, myocardial disease, pancreatitis, retroperitoneal fibrosis, sarcoidosis, Waldenström macroglobulinemia
Treatment
  • Resection, treatment of underlying conditions
Clinical images

Images hosted on other servers:

Markedly dilated lymphatics

Microscopic (histologic) images

Images hosted on other servers:

Markedly dilated lymphatics



Images contributed by Dr. Semir Vranić: