Table of ContentsDefinition / general | Treatment | Clinical images | Microscopic (histologic) images
Cite this page: Gulwani H. Lymphangiectasia. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/smallbowellymphangiectasia.html. Accessed August 6th, 2020.
Definition / general
- Primary intestinal lymphangiectasia is rare disorder of dilated intestinal lacteals resulting in lymph leakage into the small bowel lumen, causing protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia (Orphanet J Rare Dis 2008;3:5, eMedicine: Intestinal Lymphangiectasia [Accessed 12 February 2018])
- Dilation of lymphatics in mucosa, submucosa or subserosa
- Primary: children, due to congenital obstructive defective in lymphatics
- Secondary: due to constrictive pericarditis, Crohn's (Virchows Arch 2008;452:57), intestinal malignancy, myocardial disease, pancreatitis, retroperitoneal fibrosis, sarcoidosis, Waldenström macroglobulinemia
- Resection, treatment of underlying conditions