Small intestine & ampulla
Benign tumors / tumor-like conditions
Lymphangiectasia


Topic Completed: 1 August 2012

Minor changes: 14 July 2020

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PubMed Search: Lymphangiectasia[TI] small bowel[TIAB]

Hanni Gulwani, M.B.B.S.
Page views in 2019: 5,014
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Cite this page: Gulwani H. Lymphangiectasia. PathologyOutlines.com website. https://www.pathologyoutlines.com/topic/smallbowellymphangiectasia.html. Accessed August 6th, 2020.
Definition / general
  • Primary intestinal lymphangiectasia is rare disorder of dilated intestinal lacteals resulting in lymph leakage into the small bowel lumen, causing protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia (Orphanet J Rare Dis 2008;3:5, eMedicine: Intestinal Lymphangiectasia [Accessed 12 February 2018])
  • Dilation of lymphatics in mucosa, submucosa or subserosa
  • Primary: children, due to congenital obstructive defective in lymphatics
  • Secondary: due to constrictive pericarditis, Crohn's (Virchows Arch 2008;452:57), intestinal malignancy, myocardial disease, pancreatitis, retroperitoneal fibrosis, sarcoidosis, Waldenström macroglobulinemia
Treatment
  • Resection, treatment of underlying conditions
Clinical images

Images hosted on other servers:

Markedly dilated lymphatics

Microscopic (histologic) images

Images hosted on other servers:

Markedly dilated lymphatics



Contributed by Dr. Semir Vranić
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